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KMID : 0191120120270010096
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Journal of Korean Medical Science
2012 Volume.27 No. 1 p.96 ~ p.100
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Early-onset Childhood Sarcoidosis with Incidental Multiple Enchondromatosis
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Lee Jong-Hwa
Lim Yeon-Jung
Lee Seung-Hun
Joo Kyung-Bin
Choi Yun-Young
Park Chan-Kum
Lee Young-Ho
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Abstract
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The triad of rash, arthritis, and uveitis seems to be characteristic for early-onset childhood sarcoidosis. We describe an interesting case of early-onset childhood sarcoidosis coexisting enchondromatosis, which clinically masquerade as Langerhans cell histiocytosis. A 33 months old girl presented with skin rash, subcutaneous nodules with polyarthritis, and revealed the involvement of lymph nodes as well as spleen during work-up. She also presented with multiple osteolytic lesions which pathologically proven enchondromatosis. Oral prednisone was prescribed at 2 mg/kg/day for 2 months until when subcutaneous nodules and joint swellings almost disappeared, and then slowly tapered over a period of 5 months. We report an unusual case of early-onset childhood sarcoidosis presented with osteolytic bone lesions which were irrelevant to sarcoidosis.
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KEYWORD
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Sarcoidosis, Polyarthritis, Enchondromatosis, Nodule, Childhood
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